FRCS Paediatric Ortho — improved notes
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065. Enchondromatosis

visual-inline rebuild2 extracted figuresspeaker notes XML32 study lines3 Q&A

Individual slide images have been cropped from the rendered slide and inserted beside the matching note section. The full slide remains below only for layout/audit.

Clean FRCS notes with inline figures

Ollier’s disease

•Sporadic
•Defect enchondral ossification

Clinical:

•Unilateral involvement → LLD
•Angular deformity
•Ddx: fibrous dysplasia (polyostotic), OI
•XR: cartilage containing lesion + irregular translucent area at metaphysis. Expanded bone. Polyostotic
•Maffucci syndrome
•= Ollier + hemangioma
•Expanded bone
•Cutaneous haemangiomata

XR: Ollier + small rounded calcified phleboliths

Radiograph / imaging
Fig 1. Radiograph / imagingtop centre
Radiograph / imaging
Fig 2. Radiograph / imagingtop left
•Malignant transformation
•Solitary <1%
•Olliers 25-30%
•Maffucci 100%

What to consider in the treatment?

Deformity in 4 planes?

•Coronal: valgus varus
•Sagittal: flexion extension
•Transverse: torsional
•Longitudinal: LLD
•Aim to have well aligned limbs in all those planes

Options:

•Use of hemiepiphysiodesis or guided growth

Osteotomy for acute or gradual correction

•Combo of techniques
•Enchondroma = type of incomplete enchondral ossification, escape of chondroblast to metaphysis (presence of cartilage in IM canal)
•Rubin: physis hyperplasia
•Vs
•Osteochondroma= benign chondrogenic lesion derived from the perichondral ring - metaphysis hyperplasia

Direct Q&A

Q1 What are the radiographic findings for Enchondromatosis?

Malignant transformation

•Solitary <1%
•Olliers 25-30%
•Maffucci 100%
Q2 Deformity in 4 planes?

Coronal: valgus varus

•Sagittal: flexion extension
•Transverse: torsional
•Longitudinal: LLD
•Aim to have well aligned limbs in all those planes
Q3 What operative steps, indications, and risks are listed for Osteotomy for acute or gradual correction?

Combo of techniques

•Enchondroma = type of incomplete enchondral ossification, escape of chondroblast to metaphysis (presence of cartilage in IM canal)
•Rubin: physis hyperplasia
•Vs
•Osteochondroma= benign chondrogenic lesion derived from the perichondral ring - metaphysis hyperplasia

Raw speaker-note hierarchy audit

#lvlmarLindentlogicaloriginal note line
10NoneNone0Ollier’s disease
20NoneNone0Sporadic
30NoneNone0Defect enchondral ossification
40NoneNone0Clinical:
50NoneNone0Unilateral involvement --> LLD
60NoneNone0Angular deformity
70NoneNone0Ddx: fibrous dysplasia (polyostotic), OI
80NoneNone0XR: cartilage containing lesion + irregular translucent area at metaphysis. Expanded bone. Polyostotic
90NoneNone0Maffucci syndrome
100NoneNone0= Ollier + hemangioma
110NoneNone0Clinical:
120171450-1714501Expanded bone
130171450-1714501Angular deformity
140171450-1714501Cutaneous haemangiomata
150NoneNone0XR: Ollier + small rounded calcified phleboliths
160NoneNone0Malignant transformation
171NoneNone1Solitary <1%
181NoneNone1Olliers 25-30%
191NoneNone1Maffucci 100%
200NoneNone0What to consider in the treatment?
210NoneNone0Deformity in 4 planes?
220NoneNone0Coronal: valgus varus
230NoneNone0Sagittal: flexion extension
240NoneNone0Transverse: torsional
250NoneNone0Longitudinal: LLD
260NoneNone0Aim to have well aligned limbs in all those planes
270NoneNone0Options:
280171450-1714501Use of hemiepiphysiodesis or guided growth
290171450-1714501Osteotomy for acute or gradual correction
300171450-1714501Combo of techniques
310000Enchondroma = type of incomplete enchondral ossification, escape of chondroblast to metaphysis (presence of cartilage in IM canal)
320000Rubin: physis hyperplasia
330000Vs
340000Osteochondroma= benign chondrogenic lesion derived from the perichondral ring - metaphysis hyperplasia

Improved semantic hierarchy used for the study notes

#semantic levelsection?rewritten line
10Ollier’s disease
21Sporadic
31Defect enchondral ossification
40yesClinical:
51Unilateral involvement → LLD
61Angular deformity
71Ddx: fibrous dysplasia (polyostotic), OI
81XR: cartilage containing lesion + irregular translucent area at metaphysis. Expanded bone. Polyostotic
91Maffucci syndrome
101= Ollier + hemangioma
111Expanded bone
121Cutaneous haemangiomata
130yesXR: Ollier + small rounded calcified phleboliths
141Malignant transformation
151Solitary <1%
161Olliers 25-30%
171Maffucci 100%
180yesWhat to consider in the treatment?
190yesDeformity in 4 planes?
201Coronal: valgus varus
211Sagittal: flexion extension
221Transverse: torsional
231Longitudinal: LLD
241Aim to have well aligned limbs in all those planes
250yesOptions:
261Use of hemiepiphysiodesis or guided growth
270yesOsteotomy for acute or gradual correction
281Combo of techniques
291Enchondroma = type of incomplete enchondral ossification, escape of chondroblast to metaphysis (presence of cartilage in IM canal)
301Rubin: physis hyperplasia
311Vs
321Osteochondroma= benign chondrogenic lesion derived from the perichondral ring - metaphysis hyperplasia
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